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Abdominal Defect {Exomphalos}
Niraj kumar1, Shallini Gupta2, Deepak kumar1, Sanjeev Kumar Digra1, Pankaj Kumar Gupta3.
1Department of Pediatrics, Government Medical College, Jammu, India,
2Department of Pharmacology, Government Medical College, Jammu, India,
3Department of Anesthesiology, Government Medical College, Jammu, India.
ADDRESS FOR CORRESPONDENCE
Dr Niraj Kumar, Department of Pediatrics, Government Medical College, Jammu, India.
Email: nirajkdr@gmail.com
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What is the diagnosis?
Exomphalos. It encompasses a spectrum of abnormalities ranging from a small defect with the gut prolapsing into the cord {a hernia into the cord} through umbilical defects less than 5cm wide {Exomphalos minor} to larger umbilical defects {Exomphalos major or giant omphalocele}. {1} An Omphalocele is a herniation or protrusion of the abdominal contents into the base of the umbilical cord. The herniation of intestines into the cord occurs in about 1 in 5000 births and herniation of liver and intestines in 1 in 10000 births. {2} Although many are isolated defects, some are part of constellation of malformation {such as Beckwith- Weidman syndrome or Trisomy 18}, and a few are associated with maternal intake of valproic acid. {3} Prenatal ultrasound detects these defects after 14 weeks gestation as during 1st trimester midgut normally is herniated. {3,4} Surgical closure of the defect may be accomplished with a primary closure or a staged repair once the neonate is hemodynamically stable. {4} Urgent surgery is not indicated for the exomphalos with an intact amniotic sac. Ruptured exomphalos requires urgent surgery. {1}
E-published: August 2012 Vol 9 Issu 8 Art # 52 |
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Funding: None
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Conflict of Interest: None
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DOI: https://doi.org/10.7199/ped.oncall.2012.52 |
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Cite this article as:
kumar N, Gupta S, kumar D, Digra S K, Gupta P K. Abdominal Defect (Exomphalos). Pediatr Oncall J. 2012;9: 84-85. doi: 10.7199/ped.oncall.2012.52
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