Spot Diagnosis

Male Epispadias - Recognition at a glance

Machado Morais Joana1, Martins Filipa1, Coelho Ana2, Mota Céu1, Rocha Sandra1, Pinho Liliana1
1Neonatal Intensive Care Unit, Centro Materno Infantil do Norte, Porto-Portugal, 2Surgery Department, Centro Materno Infantil do Norte, Porto-Portugal

Address for Correspondence: Joana Machado Morais, Avenida da República, nº81, 4º esquerdo, Matosinhos, 4450-241, Portugal.
Email: machado_joanaf@hotmail.com
Keywords : Extrophy-Epispadias Complex, Neonatology, Pediatric Surgery
Question :
A male newborn delivered at 392/7 weeks to a 28-year-old gravida 1, para 0 woman. Pregnancy was uneventful and no fetal anomalies were detected at prenatal ultrasound. The mother underwent a cesarean section due to pelvic presentation. Apgar score was 9, 10, 10 at 1, 5, and 10 minutes, respectively. Anthropometric measurement at birth was appropriate for gestational age (weight 3090 g, head circumference 34.5 cm, length 46 cm). The postnatal exam showed a dorsally open urethral meatus with mild pubic diastasis and closed anterior abdominal wall and bladder, compatible with epispadias diagnosis. The neonate exhibited micrognathia, with no other significant abnormalities. Renal and cranial ultrasounds were normal. Genetic tests revealed a normal karyotype, but an abnormal array result (13q34x3, 16p13.3x1). During the first year, the patient will remain under surveillance, assessing bladder capacity by voiding cystourethrography and cystoscopy, whose findings will help deciding the type of surgery. The neonate will need surgical repair of epispadias and, possibly, bladder neck repair.

Figure 1. Male Epispadias.
<b>Figure 1.</b> Male Epispadias.


Figure 2. Male Epispadias.
<b>Figure 2.</b> Male Epispadias.


What is the diagnosis?
 
Disclaimer: The information given by www.pediatriconcall.com is provided by medical and paramedical & Health providers voluntarily for display & is meant only for informational purpose. The site does not guarantee the accuracy or authenticity of the information. Use of any information is solely at the user's own risk. The appearance of advertisement or product information in the various section in the website does not constitute an endorsement or approval by Pediatric Oncall of the quality or value of the said product or of claims made by its manufacturer.
0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0