Tricuspid Atresia

Tricuspid Atresia Types

• Normally related great arteries

• Small VSD & PS

• Intact ventricular septum with Pulmonary atresia

• Large VSD without pulmonary stenosis

• D-Transposition of great arteries

• VSD without pulmonary stenosis

• VSD & PS

• VSD & PA

• L-Transposition of great arteries

Presentation

Cyanosis (severe) with cyanotic spells

Physical Examination:

• Cyanosis with or without clubbing

• Systolic murmur with single S2

• Hepatomegaly with inadequate interatrial communication

Tricuspid Atresia - Investigations

• ECG: superior QRS axis, small RV forces

• Chest X-ray: Heart Size-normal, Pulmonary Vascularity - decreased

Tricuspid Atresia - Treatment

• Prostaglandin E1: 0.05 mcg/kg/min. IV infusion (to keep ductus open)

• Balloon septostomy

• Surgical:

• Palliation
• Systemic-Pulmonary shunt (PS)
• Pulmonary artery banding (large VSD)

• Corrective - Fontan's procedure